Fibrous dysplasia is a disorder where normal bone and marrow is replaced with fibrous tissue, resulting in formation of bone that is weak and prone to. Polyostotic fibrous displasia: A case report. Displasia fibrosa poliostótica: presentación de un caso. Visits. Download PDF. Carlos Francisco Meneses. Transcript of DISPLASIA FIBROSA POLIOSTOTICA. CAUSAS MUTACIONES genéticas EN EL GEN GNAS(GEN DEFECTUOSO).

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Fronto-orbital sphenoidal fibrous dysplasia. Case 2 Case 2. It may present at any age, but most commonly develops during adolescence and progresses into adulthood. An year-old girl with migrating bone pain for the last year, with normal radiographs, now poliostoyica with one month of low-degree fever.

Fibrous dysplasia of bone

Case 16 Case Colchicine use in isolated renal AA Chest and abdominal CT were unremarkable, except for the pelvic findings. You can also scroll through stacks with your mouse wheel or the keyboard arrow keys. May 8, at It should be noted that many reported cases may relate to previous treatment with radiation therapy 6. All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.

Read it at Google Books – Find it at Amazon. Case 14 Case Thank you for updating your details.


The main differential diagnosis of the monostotic form on head and neck bones is Ossifying Fibroma which some consider another form of the same entity. Case 12 Case Fibrous dysplasia is a mosaic disease resulting from post-zygotic activating mutations of the GNAS locus at 20q This page was last edited on 24 Septemberat Osteitis fibrosa cystica Brown tumor. Your email address will not be published. Case 7 Case 7.


Bone marrow stromal cells in fibrous dysplasia produce excess amounts of the phosphate-regulating hormone fibroblast growth factor FGF23leading to loss of phosphate in the urine.

Artigo recebido em 6 de setembro de Case 10 Case None of the above. Muppet did not think of it.

Ischaemia Avascular necrosis Osteonecrosis of the jaw Algoneurodystrophy Hypertrophic pulmonary osteoarthropathy Nonossifying fibroma Pseudarthrosis Stress fracture Fibrous dysplasia Monostotic Polyostotic Skeletal fluorosis bone cyst Aneurysmal bone cyst Hyperostosis Infantile cortical hyperostosis Osteosclerosis Melorheostosis Pycnodysostosis.

Langerhans cell histiocytosis 3.

Fibrous dysplasia of bone – Wikipedia

Only a few lesions can produce a sequestrum; classically, as far as I concern, basically 4: How to cite this article. Treatment in fibrous dysplasia is mainly palliative, and is focused on managing fractures and preventing deformity.

Fibrous dysplasia is a disorder where normal bone and displaasia is replaced with fibrous tissueresulting in formation of bone that is weak and prone to expansion.

Fibrous dysplasia is due to developmental dysplasia and focal arrest in normal osteoblastic activity secondary to a non-hereditary mutation which results in the presence of all of the components of normal bone with a lack of normal differentiation into their mature structures. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact.

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Solution Giuseppe Sabino says: The presence of a sequestrum and thick periosteal reaction suggests a chronic osteomyelitis. The bony trabeculae are abnormally thin and irregular, and often likened to Chinese characters bony spicules on biopsy. The long term follow up of this pacients is necessary in order to make an early diagnosis of recurrences.

Fibrous dysplasia is a pseudo-neoplastic lesion, ethiology unknown, benign and recurrent, which normal bone is replaced by fibrous tissue and lamelar bone trabeculae. Plliostotica damaged parts of your bones take up more of the tracers, which show up more brightly on the scan.

This test uses radioactive tracers, which are injected into your bloodstream. Articles needing additional references from January All articles needing additional references Infobox medical condition new.

Case 31 Case Not surprisingly, bone affected by fibrous dysplasia is weaker than normal and thus susceptible to pathological fractures. Solution Dear Dislasia, Muppet gratefully acknowledges the contribution of his good friend Dr.