Dermatol Clin. Jul;11(3) Epidermolysis bullosa acquisita and bullous systemic lupus erythematosus. Diseases of autoimmunity to type VII collagen. Bullous Systemic Lupus Erythematosus (BSLE) is a rare manifestation of . (BP), inflammatory variant of epidermolysis bullosa acquisita (EBA), and linear IgA. However, unlike epidermolysis bullosa acquisita, bullous systemic lupus erythematosus tends to respond dramatically to treatment with.

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Epidermolysis bullosa acquisita occurring in association with bullous lupus erythematosus.

Lupus Eritematoso Sistémico Bulloso en una niña de 10 años de edad. Reporte de un caso

Bullous disease in systemic lupus erythematosus. To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior. Russell’s viper venom test revealed no lupus like anticoagulant.

J Invest Dermatol, 91pp. Hulloso auto-epitopes of type VII collagen are short, paired peptide sequences within the fibronectin type III homology region of the noncollagenous NC1 domain. Bullous bullkso of systemic lupus erythematosus Dramatic response to dapsone therapy. J Am Acad Dermatol ; Arch Dermatol,pp. J Invest Dermatol, 81pp. Nephrol Dial Transplant, 14pp.

Lupus ampolloso: un verdadero reto diagnóstico y terapéutico

La respuesta al tratamiento con dapsona fue notable a las 48 horas. On examination, there were multiple, tense, clear as well as hemorrhagic, vesicles and bullosk, arising over an erythematous base and predominantly involving upper lupu [ Figure 1 ].


Systemic lupus erythematosus in a multiethnic US cohort. She had a significant anemia 8. Lupus, 12buloso. The importance of clinical and histopathological findings in confirming a diagnosis of BSLE along with the very encouraging response to dapsone therapy is highlighted.

J Am Acad Dermatol. A year-old lady, a homemaker and mother of three, presented with largely asymptomatic vesicobullous lesions 2 months durationinvolving head and neck, upper limbs, and trunk over both photo-exposed and unexposed areas.

Enero a marzoBiociencias: Ann Rheum Dis ; Detection of anti-basement membrane zone antibodies in bullous systemic lupus erythematosus. Bullous eruption of systemic lupus erythematosus. Clin Rheum Dis, 8pp. Case Report A year-old lady, a homemaker and mother of three, presented with largely billoso vesicobullous lesions 2 months durationinvolving head and neck, upper limbs, and trunk over both photo-exposed and unexposed areas.

J Invest Dermatol, 84pp.

Diagnostic immunohistochemistry of the skin, pp. Sem Cut Med Surg, 17pp. Autoantibodies to type VII collagen have heterogeneous subclass and light chain compositions and their complement-activating capacities do not correlate with the inflammatory clinical phenotype.

Whether or not BSLE is associated with systemic activity is a hotly debated topic. The patient reported three previous, spontaneous abortions, 5months gestation the last one being 6 years back. Bulla spread sign and Nikolsky sign were positive. J Invest Dermatol ; Yung A, Oakley A.

Male systemic lupus erythematosus in a latin-American inception cohort of patients. A diagnosis of bullous SLE was made. Spectrum of subepidermal immunobullous disorders seen at the National Skin Centre Singapore: Treatment of Bullous Systemic Lupus Erythematosus. X-rays of chest and involved joints were normal. Though, it may be difficult to introduce the lupud initially, as in our case; every attempt should be made to use it, as relatively low doses mg have also been shown to be efficacious. Bullous eruption of systemic lupus erythematosus: Int J Dermatol ; Indirect immunofluorescence in vesiculobullous eruption of systemic lupus erythematosus.


We report a year-old lady who presented with an extensive vesicobullous eruption on face, neck, trunk, and mucosa. J Am Acad Dermatol, 9pp.

Bullous Systemic Lupus Erythematosus

The carboxyl terminus of type VII collagen mediates antiparallel dimer formation and constitutes a new antigenic epitope for epidermolysisBullosaacquisita autoantibodies. The course of the disease is benign with remission reported in most of the cases within a year, including ours. J Am Acad Dermatol, 15pp. Bullous dermatosis and systemic lupus erythematosus in a year-old boy.

J Am Acad Dermatol, 18pp.

Epidermolysis bullosa acquisita preceding the development of systemic lupus erythematosus. Si continua navegando, consideramos que acepta su uso. Continuing navigation will bulposo considered as acceptance of this use. J Am Acad Dermatol, 21pp.